Tariq Burki, M Amjad Chaudhary, Naeem Khan.
A Case Report of Atypical Megalourethra associated with Hypospadias.
J Coll Physicians Surg Pak Jan ;10(6):224-5.

Most megalourethrae are either scaphoid or fusiform. This condition is usually associated with many congenital malformations especially urogenital and gastrointestinal. Present case report is one of the most unusual types where the entire urethra from tip of the penis right down to perineum was hypospadiac which doesn`t conform with Stephens and Fortune theory of failure of recanalization as a cause of megalourethra. The child, however, did not have any other associated abnormalities.

CASE REPORT: A two-week-old child was brought with what parents thought an abnormal penis. There were no other complaints. On examination, the child had a typical scaphoid megalourethra. There was a markedly patulous redundant hypospadiac urethra, the ventral aspect of which was missing from tip of penis to the penoscrotal junction. He was continent and urinated with a stream from urinary meatus situated in the perineum. He had normally descended testis. There were no other detectable physical abnormalities. At the age of five months , excessively redundant urethra was trimmed and repaired over a catheter of size 8 F. At the same time suprapubic diversion of urine was established with placement of vasicostomy catheter Furthermore, the redundant skin was also trimmed to provide better cosmetic appearance of the penis. Postoperative period was uneventful.

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