Khalid Maudood Siddiqui, Sobia Khan.
Anesthetic management of an infant with epidermolysis bullosa undergoing inguinal hernia repair.
J Pak Med Assoc Jan ;65(6):497-8.

Epidermolysis bullosa is a group of inherited disorders characterized by blistering of the skin as a result of minor trauma. We managed an infant with epidermolysis bullosa undergoing inguinal hernia repair. Anaesthesia was induced with oxygen/nitrous oxide mixture and sevoflurane. Oral tracheal intubation was done with a lubricated laryngoscope blade with KY jelly using atracurium 0.5mg/kg and fentanyl 0.1µgm/kg. To avoid frictions on the skin, endotracheal tube was tied with ribbon gauze and fixed around the neck. Pulse-oximetry probe and electrocardiogram electrodes were placed, and then attached to the patient`s skin covered with KY jelly. Peripheral venous access was secured in the right foot and sutured. These methods were effective to avoid new blisters and useful for infant safety.

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