Ashfaq Ahmed, Latif Khan, Muhammad Farrukh Bashir, Saeed Ahmad, Shahzad Javed, Naeem Ahmed, Amer Aziz.
Outcome Of Shish Kabab Osteotomies Fixed With Sign Naili In Osteogenesis Imperfecta. Our Experience At Ghurki Trust Teaching Hospital, Lahore, Pakistan.
Esculapio J Services Inst Med Sci Jan ;13(1):45-50.

Objective: To evaluate the results of shish kabab osteotomies fixed with SIGN NAIL in long bone deformities of patients suffering from osteogenesis imperfecta. Methods: This study was carried out on 12 patients who presented in OPD or Emergency Department with deformities of long bones. Detailed history, examination and investigations including X-ray AP and Lateral view of involved bone were done. All these cases were treated with Shish Kabab Osteotomies and SIGN NAILunder spinal or general anaesthesia. These cases were followed up for up to average of 20 months (range 06 months -6 years ) and results of the nail were observed in terms of union, rehabilitation and complications. Results: It was found that 8 (66.7%) were male and 4 (33.3%) were females with a mean age of 14.83±5.24. 5 (41.7%) patients having age 10-15 years and 7 (58.3%) were between 16-20 years. Total 21 surgeries performed. 3(25.0%) had surgery on unilateral femur,2 (16.7%) on unilateral tibia, 3(25.0%) on both unilateral tibia and femur,3 (25.0%) had surgery on bilateral tibia and 1(13.3%) with bilateral tibia and femur. The parents of all patients had a first degree consanguineous marriage. The mean hospital stay were 4.17±1.75 days. All osteotomies sites heal within 06 months, better bone densities, 1 Having recurrence of deformity and no fracture were found. Only two patients using walkers while remaining need no support for walking. Conclusion: Sign Nail along with shish kabab osteotomies in deformities of osteogenesis imperfecta is the treatment of choice. Patient rehabilitation is early, hospitalization is short, and osteotomies site healing response is good as well as decrease risk of fracture.

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