Ijaz Hussain, Shah Zeb, Mohammad Irfan, Umair Ali.
Spectrum of congenital cyanotic heart disease in Khyber Pakhtoonkhwa.
Pak Heart J Jan ;48(4):190-3.

Objectives: To study the frequency and spectrum of congenital cyanotic heart disease among patients attending pediatric cardiology department for suspected cardiac problem. Methodology: This was an observational study, conducted in Pediatric Cardiology Department Lady Reading Hospital Peshawar, from 1 September 2012 to 31 August 2013.Every patient with suspected cardiac problem was subjected to echocardiographic study to know frequency and spectrum of congenital cyanotic heart disease in these patient. Results: Total number of patient studied with congenital heart disease (CHD) was 2342. Of them 434(18.53%) were found to have cyanotic congenital heart disease (CCHD). Of these CCHD patients males were 262(60.36%). Mean age was 34.42+-30.34 months (from 1 day to 18 years). Tetrology of fallot (TOF)patients were 205(47.23%) which forms 8.8% of total CHD. 0f these TOF patients 09 were already corrected. Transposition of great arteries (TGA) was found in 83 (19.12%). Ebstein with cyanosis were found in 12(2.76%) patients. Double Outlet Right Ventricle (DORV) was found in 38 (8.75%). Total anomalous pulmonary venous drainage (TAPVD) patients were 27(6.22%). Of these supracardiac TAPVD were 15(3.45%), Cardiac TAPVD were 7(1.61%) and Infracardiac TAPVD were 5(1.15%). Pulmonary atresia with intact pulmonaryseptum was found in 15(3.4%).Single ventricle was found in 21(4.84%) patients. Eisenmenger syndrome was found in 11(2.6%). Hypoplastic left heart was foundin 14 (3.22%) and 8(1.84%) having truncusarteriosus. Conclusion: About 18% of CHD in our population comprises of CCHD. TOF is the major CCHD in our population.

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