Palwasha Gul, Muhammad Atif Naveed, Muhammad Talha Yaseen, Muhammad Omer Altaf.
Agenesis of left pulmonary artery with right sided aortic arch in adult female patient: a case report.
Pak J Radiol Jan ;29(4):262-4.

Objective: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital anomaly due to a malformation of the sixth aortic arch of the affected side during embryogenesis. The diagnosis is usually set at adolescence, however it can remain asymptomatic and late diagnosis is possible. We discuss role of cross sectional imaging of asymptomatic adult female patient with pulmonary artery agenesis. Result: We present a case of 66 years old female who was known case of pancreatic adenocarcinoma however her CT chest was done as part of staging protocol, which showed left pulmonary artery agenesis with right sided aortic arch. Conclusion. Contrast-enhanced CT is non-invasive and adequate imaging modality for diagnosis of UPAA. It can also depict associated aortic arch and congenital cardiac anomalies and help in assessing PH which can be seen in such patients. Though UPAA is rare anomaly but it should be included in the differential diagnosis of a chest radiograph with a small hyper-transradiant hemithorax.

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